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XPhen,
Tyr Maxamum

An unflavored phenylalanine- and tyrosine-free
powdered product for the dietary management of tyrosinemia type
2 in children 8 years and older and adults, including pregnant
women and women of child-bearing age.
- Phenylalanine- and tyrosine-free
- Contains a balanced mixture of all other essential and non-essential
amino acids, carbohydrate, vitamins, minerals and trace elements
- XPhen, Tyr Maxamum provides 39 g of protein equivalent per
100 g of powder
- Does not contain fat thereby allowing greater flexibility
in modifying energy intake
- Osmolality:
| |
Dilution |
|
| |
1 to 7 |
690 mOsm/kg |
| |
1 to 5 |
1000 mOsm/kg |
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Directions
for Preparation and Use
-
Maxamum must be consumed in conjunction
with natural protein, fluid and other nutrients in quantities
prescribed by a dietitian or physician to meet protein and
general nutrition requirements. Fat, carbohydrate and low protein
sources may be used to supply needed calories and to fulfill
essential fatty acid requirements.
Maxamum intake will vary depending on the age, body weight
and medical condition of the individual. Intake is adjusted
to maintain normal growth and development.
- Maxamum is best served as a chilled drink with meals. Make
a paste of the prescribed amount of powder with a small volume
of water. For accuracy, Maxamum should be weighed on a gram scale.
Gradually add sufficient water to yield the prescribed volume.
It is recommended that Maxamum initially be reconstituted at
a 1 to 7 dilution (e.g. 100 g of Maxamum and 700 mL of water).
It can however be given in a more concentrated form (e.g. at
a 1 to 5 dilution or in paste form), according to taste preferences.
Additional fluids should then be offered at the same time.
Reconstituted formula should be stored in the refrigerator
and used within 24 hours.
| Nutrients |
Per
100 g |
| Calories |
297 |
| Amino
Acids, g |
47.4 |
| Protein
Equivalent, g |
39 |
| Fat,
g |
<0.5 |
| Carbohydrate,
g |
34 |
| |
|
| Amino
Acid Profile, g |
Per
100 g |
| L-Alanine |
1.9 |
| L-Arginine |
3.5 |
| L-Aspartic
Acid |
3.3 |
| L-Cystine |
1.3 |
| L-Glutamic
Acid |
5.3 |
| Glycine |
3.3 |
| L-Histidine |
2.0 |
| L-Isoleucine |
3.1 |
| L-Leucine |
5.3 |
| L-Lysine |
4.0 |
| L-Methionine |
0.85 |
| L-Phenylalanine |
None |
| L-Proline |
3.7 |
| L-Serine |
2.3 |
| L-Threonine |
2.6 |
| L-Tryptophan |
1.0 |
| L-Tyrosine |
None |
| L-Valine |
3.4 |
| L-Carnitine |
0.02 |
| Taurine |
0.15 |
| L-Glutamine |
0.40 |
| |
|
| Vitamins |
Per
100 g |
| Vitamin
A, IU (mcg R.E.) |
2346
(710) |
| Vitamin
D3, IU (mcg) |
312
(7.8) |
| Vitamin
E, IU (mg α-T.E.) |
7.7
(5.2) |
| Vitamin
K, mcg |
70 |
| Thiamine,
mg |
1.4 |
| Riboflavin,
mg |
1.4 |
| Vitamin
B6, mg |
2.1 |
| Vitamin
B12, mcg |
3.6 |
| Niacin,
mg |
13.6 |
| Folic
Acid, mcg |
500 |
| Pantothenic
Acid, mg |
5 |
| Biotin,
mcg |
140 |
| Vitamin
C, mg |
90 |
| Choline,
mg |
321 |
| Inositol,
mg |
85.7 |
| |
|
| Minerals |
Per
100 g |
| Calcium,
mg |
670 |
| Phosphorus,
mg |
670 |
| Magnesium,
mg |
285 |
| Iron,
mg |
23.5 |
| Zinc,
mg |
13.6 |
| Manganese,
mg |
2.1 |
| Copper,
mcg |
1400 |
| Iodine,
mcg |
107 |
| Molybdenum,
mcg |
107 |
| Chromium,
mcg |
50 |
| Selenium,
mcg |
50 |
| Sodium,
mg (mEq) |
560
(24.3) |
| Potassium,
mg (mEq) |
700
(17.9) |
| Chloride,
mg (mEq) |
560
(15.8) |
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Dried Glucose Syrup, L-Lysine L-Glutamate, L-Leucine, L-Proline,
L-Arginine, Calcium Glycerophosphate, L-Valine, Glycine, Aspartic
Acid, L-Isoleucine, L-Threonine, L-Serine, L-Histidine, Tripotassium
Citrate, L-Alanine, L-Cystine, Magnesium Hydrogen Phosphate,
L-Glutamic Acid, L-Tryptophan, Sodium Chloride, L-Methionine,
Trisodium Citrate, Sugar, Choline Bitartrate, Lecithin, Magnesium
Acetate, L-Glutamine, Taurine, Tricalcium Phosphate, Ferrous
Sulphate, Ascorbic Acid, M-Inositol, Zinc Sulphate, L-Carnitine,
Nicotinamide, Manganese Sulphate, DL-Alpha Tocopheryl, Calcium
D-Pantothenate, Copper Sulphate, Pyridoxine Hydrochloride,
Thiamine Hydrochloride, Riboflavin, Vitamin A Acetate, Chromium
Sulphate, Sodium Molybdate, Potassium Iodide, D-Biotin, Sodium
Hydrogen Selenite, Vitamin K1, Vitamin
D3, Cyanocobalamin.
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