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MSUD Maxamaid

MSUD Maxamaid

A isoleucine-, leucine-, and valine-free powdered medical food for the dietary management of maple syrup urine disease (MSUD) in children aged 1 to 8 years.

Main Features
  • Isoleucine-, leucine- and valine-free
  • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements
  • MSUD Maxamaid provides 25 g of protein equivalent per 100 g of powder
  • Pleasant orange flavoured powder
  • Does not contain fat thereby allowing greater flexibility in modifying energy intake
  • Osmolality (mOsm/kg) :
    •   Dilution  
      1 to 7 680 mOsm/kg
      1 to 5 940 mOsm/kg

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Indication(s)
  • Maple Syrup Urine Disease

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Directions for Preparation and Use
  • Maxamaid must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a dietitian or physician to meet protein and general nutrition requirements. Fat, carbohydrate and low protein sources may be used to supply needed calories and to fulfill essential fatty acid requirements.

    Maxamaid intake will vary depending on the age, body weight and medical condition of the individual. Intake is adjusted to maintain normal growth and development.

  • Maxamaid is best served as a chilled drink with meals. Make a paste of the prescribed amount of powder with a small volume of water. For accuracy, Maxamaid should be weighed on a gram scale. Gradually add sufficient water to yield the prescribed volume. It is recommended that Maxamaid initially be reconstituted at a 1 to 7 dilution (e.g. 100 g of Maxamaid and 700 mL of water). It can however be given in a more concentrated form (e.g. at a 1 to 5 dilution or in paste form), according to taste preferences. Additional fluids should then be offered at the same time.

Reconstituted formula should be stored in the refrigerator and used within 24 hours.

Maxamaid Range
(Flavoured & Unflavoured)
Measure Weight
1 Cup 145 g
1/2 Cup 70 g
1/4 Cup 35 g
1 Tbsp 9 g

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Precaution
  • Must only be consumed by children with proven maple syrup urine disease while under strict medical supervision. Not intended for children under one year of age. Not suitable as a sole source of nutrition. Not for parenteral use.

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Storage
  • Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

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Nutrients
Nutrients Per 100 g
Calories 350
Amino Acids, g 28.6
Protein Equivalent, g 25
Fat, g <0.5
Carbohydrate, g 62

Amino Acid Profile, g Per 100 g
L-Alanine 1.48
L-Arginine 2.60
L-Aspartic Acid 2.17
L-Cystine 0.96
L-Glutamic Acid 2.90
Glycine 2.31
L-Histidine 1.49
L-Isoleucine None
L-Leucine None
L-Lysine 2.69
L-Methionine 0.63
L-Phenylalanine 1.75
L-Proline 2.81
L-Serine 1.73
L-Threonine 1.94
L-Tryptophan 0.77
L-Tyrosine 1.75
L-Valine None
L-Carnitine 0.02
Taurine 0.14
L-Glutamine 0.28

Vitamins Per 100 g
Vitamin A, IU (mcg R.E.) 1665 (500)
Vitamin D3, IU (mcg) 480 (12)
Vitamin E, IU (mg α-T.E.) 6.5 (4.4)
Vitamin K, mcg 35
Thiamine, mg 1.1
Riboflavin, mg 1.2
Vitamin B6, mg 1
Vitamin B12, mg 2
Niacin, mg 12
Folic Acid, mcg 150
Pantothenic Acid, mg 3.7
Biotin, mcg 120
Vitamin C, mg 135
Choline, mg 110
Inositol, mg 56

Minerals Per 100 g
Calcium, mg
810
Phosphorus, mg
810
Magnesium, mg
200
Iron, mg
12
Zinc, mg
13
Manganese, mg
1.3
Copper, mcg
2000
Iodine, mcg
90
Molybdenum, mcg
45
Chromium, mcg
45
Selenium, mcg
40
Sodium, mg (mEq)
580 (25)
Potassium, mg (mEq)
840 (22)
Chloride, mg (mEq)
450 (13)

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Ingredients

Sugar, Corn Syrup Solids, L-Lysine L-Glutamate, Citric Acid, Calcium Phosphate Dibasic, L-Proline, Trisodium Citrate, L-Arginine, Gylcine, L-Aspartic Acid, L-Threonine, L-Phenylalanine, L-Tyrosine, L-Serine, L-Histidine, L-Alanine, Magnesium Hydrogen Phosphate, Artificial Flavour, Tripotassium Citrate, Potassium Chloride, L-Cystine, L-Tryptophan, L-Methionine, Tricalcium Citrate, Choline Bitartrate, L-Glutamine, L-Glutamic Acid, L-Ascorbic Acid, Taurine, Tricalcium Phosphate, Ferrous Sulfate, M-Inositol, Zinc Sulfate, L-Carnitine, Niacinamide, DL-Alpha Tocopheryl Acetate, Cupric Sulfate, Manganese Sulfate, Calcium D-Pantothenate, Pyridoxine Hydrochloride, Thiamine Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Artificial Colors (Beta-Carotene, Beet Red), Chromium Sulfate, Folic Acid, Potassium Iodide, D-Biotin, Sodium Molybdate, Sodium Hydrogen Selenite, Phylloquinone, Vitamin D3, Cyanocobalamin.

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Ordering Information
  • For product information or to place an order please call 1-877-636-2283 or fax 514-745-6625 Monday to Friday, 8:30 to 5:00 EST

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